50405

2-Methylbutyryl-L-carnitine

≥97.0% (HPLC)

• Synonym(s): (2R)-3-Carboxy-N,N,N-trimethyl-2-(2-methyl-1-oxobutoxy)-1-propanaminium inner salt
• Empirical Formula (Hill Notation): C₁₂H₂₃NO₄
• CAS Number: 256928-75-3
• Molecular Weight: 245.32
• Beilstein: 5946881
• MDL number: MFCD11975299
• UNSPSC Code: 41116107
• PubChem Substance ID: 329757597
• NACRES: NA.26

Properties

• Product Name: 2-Methylbutyryl-L-carnitine, ≥97.0% (HPLC)
• Quality Level: 100
• Assay: ≥97.0% (HPLC)
• form: powder or crystals
• optical activity: [α]/D -20±2°, c = 0.1 in H₂O
• impurities: ≤10% water
• color: white to off-white
• storage temp.: 2-8°C
• SMILES string: C[N+](C)(C)C[C@H](OC(C(CC)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO4/c1-6-9(2)12(16)17-10(7-11(14)15)8-13(3,4)5/h9-10H,6-8H2,1-5H3/t9?,10-/m1/s1
• InChI key: IHCPDBBYTYJYIL-QVDQXJPCSA-N

Description

Biochem/physiol Actions

2-Methylbutyryl-L-carnitine is not usually detected in normal individuals. The elevation of 2-methylbutyrylcarnitine suggests a deficiency of a dehydrogenase specific for isobutyryl-CoA, important in the differential diagnosis of branched chain organic acidurias by analysis of urinary organic acids and acylcarnitines in plasma or dried blood spots.

Safety Information

• Storage Class Code: 11 - Combustible Solids
• WGK: WGK 3
• Flash Point(F): Not applicable
• Flash Point(C): Not applicable